Primary non-Hodgkin lymphoma of the larynx is rare, accounting for less than 1% of all laryngeal neoplasms. Fewer than 100 cases have been reported in the literature. This case describes a 76-year-old woman with primary non-Hodgkin lymphoma of the larynx. To our knowledge, this is the first case of primary non-Hodgkin lymphoma of the larynx reported in the Danish literature.